Goldenhar's syndrome--case report.

نویسندگان

  • Antônio Luiz Barbosa Pinheiro
  • Luciana Cavalcanti Araújo
  • Suely Baptista Oliveira
  • Maria Carmeli Correia Sampaio
  • André Carlos Freitas
چکیده

Goldenhar's syndrome is a rare condition described initially in the early 1950's. It is characterized by a combination of anomalies: dermal epibulbar cysts, auricular appendices and malformation of the ears. In 1963, Gorlin suggested the name oculo-auriculo-vertebral (OAV) dysplasia for this condition and also included vertebral anomalies as signs of the syndrome. The etiology of this rare disease is not fully understood, as it has shown itself variable genetically and of unclear causes. This work reports a case of Goldenhar's syndrome in an 11-year-old female, who presented all classical signs of this rare condition

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Oculo-auriculo-vertebral (Goldenhar's) syndrome.

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عنوان ژورنال:
  • Anales otorrinolaringologicos ibero-americanos

دوره 25 5  شماره 

صفحات  -

تاریخ انتشار 1994